Summary Hereditary spherocytosis is a common inherited disorder
that is characterized by anaemia, jaundice and splenomegaly.
It is reported worldwide and is the most common inherited
anaemia in individuals of northern European ancestry. Clinical
severity is variable with most of patients having a wellcompensated
haemolytic anaemia. Some individuals are
asymptomatic, whereas others have severe haemolytic anaemia
requiring erythrocyte transfusion. Common complications
are cholelithiasis and aplastic crises. Splenectomy is curative
and it is indicated in children with moderately-severe and severe
hereditary spherocytosis and in patients with symptoms of
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