Marzo 2018 - Volume XXXVII - numero 3
Pagine elettroniche
1Scuola di Specializzazione in Pediatria, Università della Campania “Luigi Vanvitelli”
2Scuola di Specializzazione in Pediatria, Università di Messina
3IRCCS Materno-Infantile “Burlo Garofolo”, Trieste
4UOC di Oculistica, Ospedale di Conegliano (Treviso)
5Università di Trieste
Indirizzo per corrispondenza: galdofrancesca@gmail.com
Key words: Dysarthria, Acute ophtalmoplegia, Guillain-Barré syndrome, Miller Fischer syndrome, Anti-GQ1b IgG antibody
Guillain-Barré syndrome (GBS) may follow infections such as Campylobacter jejuni, cytomegalovirus and Haemophilus influenzae infections. The paper describes two familiar cases of polyneuritis cranialis, an oculopharyngeal subtype of GBS, which appeared after β-haemolytic Group A Streptococcus (GAS) infection. The diagnosis of a variant form of GBS has been made on the basis of clinical features, albumino-cytological dissociation in the cerebrospinal fluid and the response to high-dose IVIg therapy.
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Pagine elettroniche
1UOC di Pediatria e Neonatologia, Ospedale di Ravenna, AUSL della Romagna
2Pediatra di famiglia, Bagnacavallo (Ravenna)
3UOC di Neuropsichiatria Infanzia e Adolescenza, Ambito di Lugo, AUSL della Romagna
Indirizzo per corrispondenza: claudiamuratori@libero.it
Key words: Benign paroxysmal torticollis, Dyskinesia, Recurrent stereotypic episodes
Benign paroxysmal torticollis (BPT) is a rare paroxysmal dyskinesia presenting with recurrent stereotypic episodes of torticollis. The diagnosis is primarily one of pattern recognition and exclusion of alternative conditions; other symptoms, such as vomiting, pallor and eyes' rotation, may be associated with or rapidly follow the attack, leading to misdiagnosis of this disease. The onset of the episodes usually occurs during the 2-8 months of life and may recur at varying intervals. It resolves by the age of two to three years. The paper reports the recently observed case of a 2-month-old infant with benign paroxysmal torticollis to emphasize that BPT has to be included in the differential diagnosis of acquired torticollis.
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