Gennaio 2015 - Volume XXXIV - numero 1
Pagine elettroniche
1IRCCS Materno-Infantile “Burlo Garofolo”, Trieste
2Scuola di Specializzazione in Pediatria, Università di Trieste
Indirizzo per corrispondenza: elimascheroni@virgilio.it
Key words: Turner syndrome, Electrophysiological abnormality, QT prolongation
A young woman affected by Turner syndrome undergoes periodic cardiac monitoring. Her last ECG documented QT prolongation. QT prolongation is reported in patients with Turner syndrome. This electrophysiological abnor-mality is probably due to an intrinsic defect in the regula-tion of the cardiovascular system. Although a long QT is more likely to be found in these patients, no severe life-threatening tachyarrhythmias have been described so far. Paediatricians should reassure Turner patients about the prognosis of this electrophysiological abnormality while recommending the cardiologic follow up.
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