Giugno 2011 - Volume XXX - numero 6
Pagine elettroniche ; Caso Contributivo
1Scuola di Specializzazione in Pediatria, IRCCS “Burlo Garofolo”, Università di Trieste
2UO Pediatria, Ospedale “M. Bufalini”, Cesena
3UO Medicina Trasfusionale, Ospedale “M. Bufalini”, Cesena
Indirizzo per corrispondenza: angela.decunto@libero.it
Key words: Acquired haemophilia, Paediatric age, Case report
The case of a boy who presented with an isolated gross haematuria is reported. In the previous days he referred a muscular haematoma after a minimal trauma. Coagulation studies showed a prolonged activated partial thromboplastin time (90 sec), not corrected by incubating a sample of his blood with equal volumes of normal plasma (mixing study). A factor VIII level (FVIII) less than 1% was detected and a FVIII inhibitor of 2 Bethesda unit was dosed. Steroid treatment was started with prompt resolution of “acquired haemophilia”.
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