Giugno 2009 - Volume XXVIII - numero 6

Medico e Bambino


Pagine elettroniche ; Caso Contributivo

Edema acuto emorragico della prima infanzia
(porpora di Seidlmayer)

Alessandro Tagliabue, Alberto Bettinelli, Felice Cogliati

SC di Pediatria, Ospedale S. Leopoldo Mandic, Merate (Lecco)

Indirizzo per corrispondenza: a.bettinelli@ospedale.lecco.it

ACUTE HEMORRAGIC EDEMA IN YOUNG CHILDREN (SEIDLMAYER PURPURA)

Key words: Acute hemorrhagic edema, Young children, Vasculitis small vessel

Acute hemorrhagic edema is an uncommon leukocytoclastic small-vessel vasculitis that may affect young children. In literature only few cases have been reported (294 cases). In many cases the disease developed after a simple acute infection. The exanthema includes large, round, red to purpuric plaques predominant over the cheeks, ears and extremities and often tender edema of face. Involvement of body systems is rare. The children recover spontaneously without sequelae. We report a case of a 9-month boy, who presented with cockade purpura one week after gastroenteric infection. This is the second case described in our pediatric division in 33 years.

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A. Tagliabue, A. Bettinelli, F. Cogliati
Edema acuto emorragico della prima infanzia ; (porpora di Seidlmayer)
Medico e Bambino 2009;28(6):393-394 https://www.medicoebambino.com/?id=0906_393.pdf


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