Settembre 2007 - Volume XXVI - numero 7

Medico e Bambino


Pagine elettroniche ; Caso Contributivo

Ipertensione endocranica idiopatica (pseudotumor cerebri) in una bambina in terapia con ormone della crescita

G. Tornese, F. Patarino, S. Pensiero1, F. Parentin1, E. Faleschini2, G. Tonini2, F. Marchetti Clinica Pediatrica,

1Servizio di Oculistica, IRCCS “Burlo Garofolo”, Trieste;
2Servizio di Endocrinologia e Diabetologia Pediatrica, IRCCS “Burlo Garofolo”, Trieste

Indirizzo per corrispondenza: marchetti@burlo.trieste.it

IDIOPATHIC INTRACRANIAL HYPERTENSION (PSEUDOTUMOR CEREBRI) IN A GIRL RECEIVING GROWTH HORMONE TREATMENT

Key words: Idiopathic intracranial hypertension, rhGH, Acetazolamide, Corticosteroids

We report a case of idiopathic intracranial hypertension (IIH) (pseudotumor cerebri) following treatment with recombinant growth hormone (rhGH). A 9-year-old girl, treated for GH deficiency, developed bitemporal worsening headache, diplopia, intermittent exotropia and visual loss 3 months after starting rhGH. Ocular fundus examination revealed bilateral papilloedema and a MRI scan ruled out intracranial disease (including venous sinus thrombosis), leading to diagnosis of IIH. rhGH was discontinued and acetazolamide therapy was initiated up to 30 mg/kg/die dose without clinical improvement and with mild metabolic acidosis. We reduced acetazolamide to 20 mg/kg/die and added dexamethasone ev (0,4 mg/kg/die) with dramatic answer already after 1 day, then confirmed by fundus oculi and visual evocated potential. We suggest the use of corticosteroids in IIH when acetazolamide is inefficient or intolerable.

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G. Tornese, F. Patarino, S. Pensiero, F. Parentin, E. Faleschini, G. Tonini, F. Marchetti
Ipertensione endocranica idiopatica (pseudotumor cerebri) in una bambina in terapia con ormone della crescita
Medico e Bambino 2007;26(7):459-461 https://www.medicoebambino.com/?id=0707_459.pdf


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