Incidenza e storia naturale della PFAPA in Friuli-Venezia Giulia: una ricerca collaborativa dei PdF
GIANCARLO BESOLI E GRUPPO DI STUDIO SULLA PFAPA DEL FRIULI-VENEZIA GIULIA; Egidio Barbi1, Giancarlo Besoli, Laura Brusadin, Gabriella Cescato, Magda di Comun, Piero Iaschi, Lorena Loschi, Carmen Mazzolini, Giorgio Mussi, Marilena Pavoni, Mariagrazia Pizzul, Alda Predotto, Francesco Romanello, Daniele Rosenwirth, Raffaella Servello, Angelo Tarchino, Lidia Tion, Antonella Ulliana, Alessandro Ventura1, Oscar Volpi
Through a review of all cases seen during the last 5 years, 20 practicing paediatricians
were able to identify 40 cases who satisfy the diagnostic criteria for FPAPA. Recurrence
range was between 3 and 6 weeks and overall duration from 1 to 6 years. 12 cases were
successfully treated with a single dose of steroids, 12 underwent surgery and were all cured,
1 was treated with inhalatory steroids and recovered. The remaining 12 recovered
spontaneously.