BECKWITH-WIEDEMANN SYNDROME. MACROGLOSSIA AND CRANIOFACIAL GROWTH: REMARKS AND PROPOSALS

Key words: Beckwith-Wiedemann syndrome, Macroglossia, Infantile deglutition, Orthognatodontics

Description of a Beckwith-Wiedemann syndrome case (annular hernia with rectal diastase; neonatal visceromegaly, then regressed; macrosomia, then regressed; macroglossia; other minor anomalies). This case is peculiar because it is relatively not serious. The patient can have an almost normal life, the most important problem to be solved, from a practical point of view, being macroglossia.